Congenital conditions associated with Bertolotti’s Syndrome

Several congenital conditions have been observed in patients diagnosed with Bertolotti’s Syndrome. Based on currently available literature, the co-incidence of these congenital conditions and BSy is purely correlative; neither causative links nor commonalities in the genetic changes leading to these conditions has been found.

Hypermobility Ehlers-Danlos Syndrome

  • hEDS is a rare heritable tissue disorder that causes general joint hypermobility. It is the most common type of EDS, accounting for about 90% of cases.

  • Some patients with hEDS have also been shown to have Craniocervial Instability (CCI) and Thoracic Outlet Syndrome. Depending on the severity of these conditions, additional corrective surgery may be required.

  • The specific genes that cause hEDS have not been identified. As such, there is no laboratory test that can definitively identify patients with hEDS.

  • There is a high bar for diagnosis of hEDS. This is outlined in detail on the The Ehlers-Danlos Society website

Spina Bifida Occulta

  • Spina bifida is a rare congenital disorder where the spine develops abnormally during fetal development.

  • Spina bifida occulta is a mild version of this condition where a gap is present between the vertebrae of the spine.

  • This condition can be diagnosed in adults using X-Ray, MRI, or CT imaging.

  • Further information on this condition can be found in detail on the Cleveland Clinic website.

Extra L6 vertebra

  • Normally, individuals have 5 lumbar segments (top). In some people, there is an extra lumbar segment (bottom).

Cervical stenosis

  • Cervical stenosis is caused by the narrowing of the spinal canal in the cervical spine (i.e., the neck area)

  • Cervical stenosis can be congenital (i.e., present from birth) or acquired (degenerative changes after birth.

  • This condition can be diagnosed in adults using X-Ray, MRI, or CT imaging.

  • Further information on this condition can be found in detail on the Cleveland Clinic website.